Double Outlet Right Ventricle-DORV

Double Outlet Right Ventricle (DORV) is a congenital heart defect characterized by abnormal positioning of the major arteries that arise from the heart. In this condition, both the aorta and the pulmonary artery, the two main blood vessels that carry blood away from the heart, are connected to the right ventricle instead of each being connected to their respective ventricles. This leads to oxygen-rich and oxygen-poor blood mixing within the heart, resulting in insufficient oxygenation of the body’s tissues.

Understanding the Anatomy:

To understand DORV, it’s essential to grasp the normal anatomy of the heart. In a healthy heart, the aorta arises from the left ventricle and carries oxygen-rich blood to the body, while the pulmonary artery arises from the right ventricle and carries oxygen-poor blood to the lungs.

Types of DORV:

DORV is classified into different types based on the position of the two great arteries and the presence or absence of associated defects. The primary types include:

  1. DORV with subaortic VSD (ventricular septal defect): In this type, the ventricular septal defect is located beneath the aortic valve.

  2. DORV with subpulmonary VSD: Here, the ventricular septal defect is positioned beneath the pulmonary valve.

  3. DORV with doubly committed VSD: In this type, the ventricular septal defect is positioned directly between the aorta and the pulmonary artery.

Each type presents unique challenges and may require specific treatment approaches.

Symptoms and Diagnosis:

The symptoms of DORV vary depending on the severity of the defect and the presence of associated heart abnormalities. Common symptoms include:

  • Cyanosis (bluish discoloration of the skin)
  • Rapid breathing
  • Poor feeding and growth
  • Fatigue
  • Heart murmur

Diagnosis of DORV often occurs during prenatal ultrasound or shortly after birth through echocardiography. Additional imaging tests such as MRI or CT scans may be conducted to assess the heart’s structure and function more comprehensively.

Treatment Options:

Treatment for DORV aims to correct the underlying heart defect and improve heart function. The approach depends on several factors, including the type of DORV, the presence of associated defects, and the overall health of the patient. Treatment options may include:

  1. Surgical Repair: Most cases of DORV require surgical intervention to redirect the blood flow and close the ventricular septal defect. The timing of surgery depends on the severity of the condition and the presence of associated complications.

  2. Cardiac Catheterization: In some cases, minimally invasive procedures such as cardiac catheterization may be used to repair certain types of DORV or to improve blood flow within the heart.

  3. Medications: Medications may be prescribed to manage symptoms, control blood pressure, or prevent complications such as heart failure or arrhythmias.


The prognosis for individuals with DORV varies depending on factors such as the type and severity of the defect, the presence of associated abnormalities, and the timing and success of surgical intervention. With advancements in medical technology and surgical techniques, many individuals with DORV can lead fulfilling lives with appropriate treatment and ongoing medical care.

Discover world-class medical care and cultural wonders.

Contact us today and start your healing journey!